Título

PIGMENTED PARAVENOUS RETINOCHOROIDAL ATROPHY: THE IMPORTANCE OF THE RIGHT DIAGNOSIS.

Introdução / Purpose

Describe clinical alterations presented in a case of Pigmented Paravenous Retinochoroidal Atrophy, with inicial diagnosis of Retinitis Pigmentosa.

Material e Método / Methods

Case report of one case.

Resultados / Results

Female patient, 59 years old, with photophobia complaint beginning 30 years ago. The patient did not present systemic alterations, denied family history, but related a diagnosis of glaucoma, and using 03 hypotensive eye drops, with reports of eyes’s presorptive peaks of 30mmHg. She had good visual acuity, with 20/20 in right eye and 20/25 in the left eye. Fundus examination showed retinal pigmented epithelium atrophy with bone spicule pigment deposition along retinal veins. Autofluorescence (FAF), Optical Coherence Tomography (OCT) have been performed. The patient had previous Humphrey perimetry and full field ERG.

Discussão e Conclusões / Discussion

PPRCA is a rare disease, and it is necessary to have attention to the differential diagnosis, because it is not a hereditary disease like Retinitis Pigmentosa. In this case, a mistake in the diagnosis caused a concern in the patient’s family.

Palavras Chave

Pigmented Paravenous Retinochoroidal Atrophy (PPRCA); Retina.