Título

POSTERIOR POLAR ANNULAR CHOROIDAL DISTROPHY: CASE REPORT

Introdução / Purpose

Report a posterior polar annular choroidal distrophy case.

Material e Método / Methods

Retinography (photos 1 and 2)
Fluorescente retinography (photos 3 and 4)

Resultados / Results

Female patient, caucasian, 71 years old, was fowarded from other service to perform a posterior capsulotomy YAG laser treatment in both eyes. She was submitted to phacoemulsification in 2012 and in the ophthalmologic examination,she presented corrected visual acuity of 20/200 in the right eye and 20/80 in the left eye . In the biomicroscopic examination there was a posterior capsule opacity, centered and well posicioned intraocular lens (IOL) and intraocular pressure of 13 mmHg in both eyes. Indirect binocular ophthalmoscopy visualised an annular atrophy wich extended around the peripapilar area and surrounded the vascular arcades with a heavy multifocal pigmentation. There was a relative sparing of the fovea (photo 1 and 2). The fluorescente retinography showed peripapilar and vascular arcades annular hipofluorescence areas due to a window defect. A fringe of preserved choriocapillaris beneath atrophic pigment epithelium may be seen in the central macular as hyperfluorescence (photo 3 and 4).

Discussão e Conclusões / Discussion

The Posterior Polar Annular Choroidal Distrophy is a rare disease that affects areas of the vascular arcade creating an arc pattern(1) . Some studies demonstrates a progression of the atrofic area of the RPE and lost of the photoreceptors at the fovea zone (2). Differential diagnosis included Choroideremia, Gyrate Atrophy, Posterior Polar Hemispheric Choroidal Dystrophy, Central and Peripheral Annular Choroidal Distrophy (3). Patients may have progressive peripheral and central vision loss (3). There is no standard treatment protocol (3).

Palavras Chave

CHOROIDAL DISTROPHY;